#Congenital aural atresia skin

Options for hearing rehabilitation in aural atresia include surgical reconstruction of the EAC (atresiaplasty) and/or use bone anchored hearing devices.Ītresiaplasty success is predicated upon favorable anatomy, Early interventions to rehabilitate hearing are critical to speech and language acquisition. Although often sporadic, congenital aural atresia can be associated with other craniofacial abnormalities, notably those seen in Treacher-Collins and Goldenhar syndromes. Congenital aural atresia occurs in 1 in 10,000 births, typically occurring unilaterally and has a greater incidence in males. Incomplete canalization of the temporal bone during development can cause congenital aural atresia, characterized by a complete absence of the external auditory canal (EAC), with frequently associated abnormalities of the ossicular chain and a maximal conductive hearing loss. Keywords: Aural Atresia mBHAD Surgical Non Surgical Options Bone Anchored Hearing Age and Length.

#Congenital aural atresia skin

Despite lack of an external abutment, skin complications with mBAHD are common and may be mitigated by prompt evaluation and use of the lowest feasible magnet strength. Slightly improved aided WRS was seen in the soft band cohort. Interventions included decreasing magnet strength, adding soft pads, topical and oral antibiotics, and reducing device usage.Ĭonclusions: mBAHD are effective for auditory rehabilitation in pediatric congenital aural atresia with equivalent aided gain in SRT to soft band devices. MBAHD cohort (p=0.004) with four cases of persistent pain and erythema, and two cases of pain alone limiting device use. Skin complication rate was 0% in the soft band cohort and 54.5% However, the mean (SD) aided unilateral WRS was higher in the soft band group: 83.9% versus 71.2% in the mBAHD group (p=0.023).

The mean aided gain in the speech reception threshold (SRT) was similar between groups (p=0.55). Results: Age, length of follow-up (mean=28.2 months, range: 13-43 months), and bone conduction thresholds for the atretic ear were comparable between groups (p>0.05). The Cochlear™ Baha Attract system (Cochlear Americas, Centennial, CO) mBAHD (n=11) was compared to the nonsurgical softband BAHD (n=11) in terms of aided and unaided hearing thresholds, aided word recognition scores (WRS), and device related complications. Methods: Retrospective cohort study at a tertiary referral center of pediatric patients with conductive hearing loss from congenital aural atresia. Objective: To compare audiologic outcomes and skin related complications in children with aural atresia treated with non-surgical softband or transcutaneous magnet-based implantable bone anchored hearing devices (mBAHD). This work is licensed under a Creative Commons Attribution 4.0 International License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. Bone Anchored Hearing in Children with Aural Atresia: A comparison of outcomes with Transcutaneous Magnetic Surgical and non-surgical options.Ĭopyright: © 2018 The Author(s).

*Corresponding author: Maura K Cosetti, Department of Otolaryngology Head and Neck Surgery, Short Running Head: Outcomes of Magnetic Bone Anchored Hearing Aids in Pediatric Aural Atresiaĭouglas M Worrall 1, Sida Chen 1, Randi Tepper 2, George Wanna 2 and Maura K Cosetti 2*ġDepartment of Otolaryngology Head and Neck Surgery, Icahn School of Medicine at Mount Sinai, Mount Sinai Health System, New York, USAĢEar Institute, New York Eye and Ear of Mount Sinai, Mount Sinai Health System, New York, USA Bone Anchored Hearing in Children with Aural Atresia: A Comparison of outcomes with Transcutaneous Magnetic Surgical and Non-surgical Options